The clinical approach to lung disease in patients with cystic fibrosis
UMass Chan Affiliations
Department of PediatricsDocument Type
Journal ArticlePublication Date
2009-09-18Keywords
Cystic FibrosisHumans
Lung Diseases
Personal Autonomy
Practice Guidelines as Topic
Quality of Life
Respiratory Function Tests
Respiratory Therapy
Respiratory Tract Infections
Allergy and Immunology
Pediatrics
Respiratory Tract Diseases
Metadata
Show full item recordAbstract
There is strong evidence that early, aggressive therapy of lung disease leads to improved quality and quantity of life for patients with cystic fibrosis (CF). The treatment of pulmonary disease associated with CF is multifactorial, encompassing prophylaxis, aggressive treatment of infection, use of antiinflammatory agents, and treatment of severe complications. Chest physiotherapy on a regular basis, perhaps using new modalities that allow patient autonomy, is also crucial. This review covers the pathogenesis of CF lung disease and current approaches to therapy, highlighting guidelines recently published by the Cystic Fibrosis Foundation. Clinicians caring for patients with CF should maximize current therapies with the goal of preserving lung function until the time a more definitive curative or controller medication is developed. Empowering patients in the process of providing their own care is a key to achieving this goal.Source
Semin Respir Crit Care Med. 2009 Oct;30(5):505-13. Epub 2009 Sep 16. Link to article on publisher's siteDOI
10.1055/s-0029-1238909Permanent Link to this Item
http://hdl.handle.net/20.500.14038/43829PubMed ID
19760538Related Resources
Link to Article in PubMedae974a485f413a2113503eed53cd6c53
10.1055/s-0029-1238909